Menieres disease
Meniereโs Disease ๐ง๐ช๏ธ:
A rare, progressive inner ear disorder causing recurrent attacks of vertigo ๐, fluctuating sensorineural hearing loss ๐ง, and tinnitus ๐ ยฑ aural fullness.
Typically presents in middle age and can have a major impact on quality of life.
About โน๏ธ
- Characterised by endolymphatic hydrops ๐ง (raised endolymph pressure in the inner ear).
- Classical triad: vertigo ๐ + tinnitus ๐ + fluctuating hearing loss ๐ง.
- May progress to permanent sensorineural hearing loss โ๐.
Aetiology ๐งฌ
- Excess endolymph production / impaired absorption.
- Possible autoimmune ๐ค, viral ๐ฆ , or genetic ๐ช predisposition.
Clinical Features ๐
- Recurrent vertigo ๐ (20 mins โ 24 hrs).
- Fluctuating tinnitus ๐ (often roaring/ringing).
- Progressive unilateral SNHL ๐ง (may โ bilateral).
- Aural fullness/pressure ๐.
- Onset usually in middle age ๐ต, unpredictable course.
Diagnostic Criteria ๐งพ
- Vertigo ๐: โฅ2 spontaneous episodes, each lasting 20 minsโ24 hrs.
- Tinnitus ๐ / aural fullness ๐: Patient perception during attacks.
- Hearing loss ๐ง: Audiometry confirms sensorineural pattern.
Stages of Disease ๐
- Early ๐ข: Sudden vertigo attacks, fluctuating hearing, tinnitus, aural fullness.
- Middle ๐ก: Vertigo persists, hearing loss more constant, tinnitus worsens.
- Late ๐ด: Permanent hearing loss, chronic imbalance ๐คธโโ๏ธ (esp. in dark), tinnitus persists.
Differentials ๐
- BPPV ๐ข (brief vertigo, seconds).
- Vestibular migraine ๐คฏ.
- Vestibular schwannoma ๐ง๐๏ธ.
- Labyrinthitis / vestibular neuritis ๐ฆ .
- Autoimmune inner ear disease ๐งฌ.
Investigations ๐งช
- Audiometry ๐ง: Fluctuating SNHL.
- MRI ๐งฒ: Exclude acoustic neuroma.
- Vestibular tests โ๏ธ: Show unilateral hypofunction.
Management ๐
- ENT referral ๐จโโ๏ธ: Formal audiology & diagnosis confirmation.
- Acute ๐:
- Prochlorperazine ๐, cinnarizine, cyclizine, or promethazine for vertigo/nausea ๐คข.
- Severe attacks โ IV sedatives + fluids ๐.
- Long-term ๐ฟ:
- Betahistine ๐: Can reduce frequency/severity.
- Avoid triggers โ๐ท๐ง (caffeine, alcohol, excess salt).
- Self-care ๐ : vertigo precautions, avoid driving ๐ during frequent attacks.
- Support โค๏ธ: Tinnitus counselling, hearing aids, psychological support.
References ๐
๐ก Clinical Pearls
- Triad ๐๐๐ง = Mรฉniรจreโs until proven otherwise.
- Vertigo much longer (20 minsโhours โฑ๏ธ) than BPPV (seconds โฒ๏ธ).
- Late disease: hearing loss + imbalance persist, even if vertigo settles.